peeling skin syndrome
Peeling skin syndrome (PSS) refers to a group of rare autosomal recessive forms of ichthyosis that is characterized clinically by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalized distribution (generalized PSS type A (non inflammatory) or B (inflammatory)). Some cases remain difficult to classify, suggesting that there could be additional subtypes of PSS.
MONDO:0015947
inherited ichthyosis
is_a
PSS
exact
deciduous skin
exact
familial continuous skin peeling
related
familial continuous skin peeling syndrome
exact
idiopathic deciduous skin
exact
keratosis exfoliativa congenita
exact
peeling skin disease
exact
skin peeling syndrome
related