hepatic veno-occlusive disease-immunodeficiency syndrome
Hepatic veno-occlusive disease-immunodeficiency syndrome is characterized by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centers, absent tissue plasma cells and hepatic veno-occlusive disease.
MONDO:0003778
inborn error of immunity
is_a
MONDO:0003847
hereditary disease
is_a
MONDO:0019514
hepatic veno-occlusive disease
is_a
VODI
related
VODI syndrome
exact
familial veno-occlusive disease with immunodeficiency
related
hepatic veno-occlusive disease with immunodeficiency
related
hepatic venoocclusive disease with immunodeficiency
related
veno-occlusive disease and immunodeficiency syndrome
related