primary myelofibrosis
Myelofibrosis with myeloid metaplasia is a myeloproliferative disease with annual incidence of approximately 1 case per 100,000 individuals and age at diagnosis around 60 (an increased prevalence is noted in Ashkenazi Jews). Clinical manifestations depend on the type of blood cell affected and may include anemia, pallor, splenomegaly, hypermetabolic state, petechiae, ecchymosis, bleeding, lymphadenopathy, hepatomegaly, portal hypertension.
MONDO:0015610
acquired aplastic anemia
is_a
MONDO:0020076
myeloproliferative neoplasm
is_a
AMM
exact
Agnogenic myeloid metaplasia
exact
CIMF
exact
chronic idiopathic myelofibrosis
exact
idiopathic bone marrow fibrosis
exact
idiopathic myelofibrosis
exact
myelofibrosis with myeloid metaplasia
narrow
myelofibrosis with myeloid metaplasia, somatic
exact
myelofibrosis, somatic
exact
myeloid metaplasia
related
myelosclerosis with myeloid metaplasia
exact
osteomyelofibrosis
exact
primary myelofibrosis
exact