tricuspid atresia
Tricuspid atresia is (TA) a rare congenital heart malformation characterized by the congenital agenesis of tricuspid valve leading to severe hypoplasia of right ventricle (functionally univentricular). TA is associated with normally related or transposed great vessels (TGV), an obligatory interatrial connection that is crucial for survival (patent foramen ovale or atrial septal defect, osteum secondum type), ventricular septal defect (in 90% cases), pulmonary outflow obstruction - pulmonary atresia, stenosis or hypoplasia (usually in TA with normally related vessels but also in TGV), aortic coarctation and/or aortic arch interruption (usually in TA with TGV).
MONDO:0005453
congenital heart disease
is_a
MONDO:0020289
congenital tricuspid malformation
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MONDO:0100547
cardiogenetic disease
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congenital agenesis of the tricuspid valve
related
congenital atresia of tricuspid valve
exact
tricuspid atresia
exact
tricuspid atresia (disease)
exact
tricuspid valve atresia
exact