nephrotic syndrome, type 4
Nephrotic syndrome within the first three motnhs of life, characterized initially by increased mesangial matrix, with or without hypertrophy and hyperplasia of podocytes, and eventual glomerular sclerosis.
MONDO:0002350
familial nephrotic syndrome
is_a
DMS
related
NPHS4
related
WT1 nephrotic syndrome
exact
congenital nephrotic syndrome - diffuse mesangial sclerosis
exact
diffuse isolated mesangial sclerosis
related
diffuse mesangial sclerosis
related
familial mesangial sclerosis
related
isolated diffuse mesangial sclerosis
related
mesangial sclerosis, diffuse
related
nephrotic syndrome caused by mutation in WT1
exact
nephrotic syndrome, early onset with diffuse mesangial sclerosis
related
nephrotic syndrome, type 4
exact