nodular cutaneous amyloidosis
Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as SjC6grenBs syndrome and CREST syndrome.
MONDO:0015301
primary cutaneous amyloidosis
is_a
NLCA
related
PLCNA
exact
amyloidosis cutis nodularis atrophicans
related
amyloidosis nodular localised cutaneous
exact
amyloidosis nodular localized cutaneous
exact
primary localised cutaneous nodular amyloidosis
exact
primary localized cutaneous nodular amyloidosis
exact