hereditary clear cell renal cell carcinoma
A manifestation of von Hippel-Lindau disease or other familial renal cell cancer syndromes that present as a malignant epithelial neoplasm of the kidney. It is characterized by the presence of lipid-containing clear cells within a vascular network. The tumor usually is bilateral and polycentric, and metastasizes to unusual sites. Late metastasis is common.
MONDO:0003008
hereditary renal cell carcinoma
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MONDO:0005005
clear cell renal carcinoma
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Hereditary clear cell renal cell cancer
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hereditary clear cell renal carcinoma
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hereditary clear cell renal cell adenocarcinoma
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hereditary clear cell renal cell carcinoma
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hereditary conventional (clear cell) renal cell carcinoma
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