Thiemann disease, familial form
Thiemann disease is a very rare genetic necrotic bone disorder characterized clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.
MONDO:0018381
osteochondrosis
is_a
MONDO:0018383
osteonecrosis of genetic origin
is_a
Osteochondrosis of phalangeal epiphyses
exact
Thiemann's disease
related
aseptic necrosis of phalangeal epiphyses
exact
osteoarthropathy of fingers familial
related
osteochondritis of phalangeal epiphyses
exact