glaucoma secondary to spherophakia/ectopia lentis and megalocornea
Glaucoma secondary to spherophakia/ectopia lentis and megalocornea is a rare, genetic, non-syndromic developmental defect of the eye disorder characterized by congenital megalocornea associated with spherophakia and/or ectopia lentis leading to pupillary block and secondary glaucoma. Additional features may include flat irides, iridodonesis, axial myopia, very deep anterior chambers, miotic, oval pupils without well-defined borders, ocular pain and irritability manifesting as conjunctival injection, corneal edema and central scarring, as well as a high arched palate.
MONDO:0009633
microspherophakia and/or megalocornea, with ectopia lentis and with or without secondary glaucoma
is_a
MONDO:0018174
hereditary glaucoma
is_a
megalocornea-spherophakia-secondary glaucoma syndrome
exact