intravascular large B-cell lymphoma
Intravascular large B-cell lymphoma (IVLBCL) is a very rare form of diffuse large B-cell lymphoma characterized by the selective growth of lymphoma cells within the lumina of small blood vessels (especially the capillaries) that most often presents with a wide range of clinical manifestations (as potentially any tissue can be involved), with patients from Western countries more frequently manifesting with neurological and cutaneous symptoms while patients from Asian countries more frequently displaying hepatosplenomegaly and thrombocytopenia. IVLBCL is characterized by an absence of lymphadenopathy, an aggressive clinical course and a poor prognosis.
MONDO:0018905
diffuse large B-cell lymphoma
is_a
IVBCL
related
Tappeiner-Pfleger disease
exact
angioendotheliomatosis proliferans systemisata
exact
angiotropic large cell lymphoma
exact
angiotropic lymphoma
exact
intravascular B-cell lymphoma
exact
intravascular large B-cell lymphoma
exact
intravascular lymphomatosis
exact
malignant angioendotheliomatosis
exact