isolated right ventricular hypoplasia
Isolated right ventricular hypoplasia (IRVH) is a rare congenital heart malformation characterized by underdevelopment of the right ventricle associated with patent foramen ovale or interauricular communication and normally developed tricuspid and pulmonary valves. IRVH manifests with severe cyanosis, congestive heart failure, and in severe cases, death in early infancy.
MONDO:0003847
hereditary disease
is_a
MONDO:0020291
hypoplastic right heart syndrome
is_a
hypoplasia of the right ventricle
related
isolated hypoplasia of the right ventricle
related
right ventricle hypoplasia
related
right ventricular hypoplasia
related