small intestinal enteropathy-associated T-cell lymphoma
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate.
MONDO:0000621
immune system cancer
is_a
MONDO:0001852
small intestine lymphoma
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MONDO:0004805
leukocyte disorder
is_a
MONDO:0019473
enteropathy-associated T-cell lymphoma
is_a
enteropathy-associated T-cell lymphoma of small intestine
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small intestinal EATL
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small intestinal enteropathy-type T-cell lymphoma
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small intestine enteropathy-associated T-cell lymphoma
exact