pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
A rare subgroup of pulmonary arterial hypertension (PAH) characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction.
MONDO:0005087
respiratory system disorder
is_a
MONDO:0015924
pulmonary arterial hypertension
is_a
PVOD and/or PCH
exact