letterer-Siwe disease
A multifocal, multisystem form of Langerhans-cell histiocytosis. There is involvement of multiple organ systems including the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia.
MONDO:0017025
Langerhans cell histiocytosis specific to childhood
is_a
acute and disseminated Langerhans cell histiocytosis
exact
acute disseminated Langerhans cell histiocytosis
exact
letterer-Siwe disease
exact
multifocal multisystem Langerhans cell histiocytosis
exact