linear and whorled nevoid hypermelanosis
Linear and whorled nevoid hypermelanosis (LWNH) is a rare skin condition characterized by swirling streaks of hyperpigmented (darkened) skin. The pigmentation follows the lines of Blashko and is mainly located on the trunk and limbs. It is present at birth or appears in the first few weeks of life. It typically progresses for one to two years and then stabilizes. Hyperpigmentation is usually the only symptom but there are isolated reports of other symptoms, involving mostly the central nervous system, musculoskeletal system, and heart. While most cases of LWNH are sporadic, apparent genetic transmission rarely has been described. A few people with LWNH have been diagnosed with chromosomal mosaicism.
MONDO:0006499
hamartoma
is_a
MONDO:0011500
Becker nevus syndrome
is_a
MONDO:0019289
hyperpigmentation of the skin
is_a
Becker Nevus
exact
Becker's Nevus
exact
LWNH
related
linear and whorled hypermelanosis
related
linear papular ectodermal-mesodermal hamartoma
exact
melanosis Neviformis
exact
nevoid hypermelanosis, linear and whorled
related
pigmented hairy Epidermal Nevus
exact
pigmented hairy Nevus of Becker
exact
progressive cribriform and zosteriform hyperpigmentation
exact
reticulate hyperpigmentation of Iijima
related
zebra-like hyperpigmentation
related
zosteriform hyperpigmentation
related
zosteriform lentiginous nevus
related