isolated congenital hepatic fibrosis
A congenital disorder usually inherited in an autosomal recessive pattern. It affects the hepatobiliary system and the kidneys. It is characterized by liver fibrosis, portal hypertension, and renal cysts.
MONDO:0004868
biliary tract disorder
is_a
MONDO:0007329
cirrhosis, familial
is_a
Congenital Hepatic Fibrosis
exact
congenital fibrose liver
related
congenital hepatic fibrosis
exact
isolated CHF
broad
nonsyndromic congenital hepatic fibrosis
exact