clear cell sarcoma of kidney
A rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It is associated with internal tandem duplications in the BCOR gene. It metastasizes to lung, bone, brain and soft tissue.
MONDO:0015963
obsolete inherited renal tumor (obsolete MONDO:0015963)
excluded_subClassOf
MONDO:0002926
clear cell sarcoma
is_a
MONDO:0002930
kidney sarcoma
is_a
CCSK
exact
childhood clear cell sarcoma of the kidney
exact
childhood kidney clear cell sarcoma
exact
childhood renal clear cell sarcoma
exact
clear cell sarcoma - kidney
exact
clear cell sarcoma of kidney
exact
clear cell sarcoma of the kidney
exact
kidney clear cell sarcoma
exact
paediatric kidney clear cell sarcoma
exact
paediatric renal clear cell sarcoma
exact
pediatric kidney clear cell sarcoma
exact
pediatric renal clear cell sarcoma
exact
renal clear cell sarcoma
exact