extranodal nasal NK/T cell lymphoma
A rare, malignant neoplasm mainly affecting men in the fifth decade of life, that usually arises in the nose, paranasal sinuses, orbits or upper airway, and that can present with a nasal mass, nasal bleeding, nasal obstruction, palate perforation (i.e. midline perforation of the hard palate), and mid-facial and/or upper airway destructive lesions. In advanced disease stages, which are associated with a poor prognosis, NKTCL may disseminate to other organs. A few cases of NKTCL presenting primarily in the lymph nodes have also been described.
MONDO:0005062
lymphoma
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MONDO:0017343
Epstein-Barr virus-associated lymphoproliferative disorder
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Extranodal NK/T lymphoma-nasal
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Extranodal NK/T-cell lymphoma, nasal type
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NK/T-cell lymphoma
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NKTCL
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angiocentric T-cell lymphoma
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lethal midline granuloma
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nasal T/natural killer-cell lymphoma
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nasal type Extranodal NK/T-cell lymphoma
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reticulosis, malignant
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