congenital fibrosarcoma
A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes.
MONDO:0002677
conventional fibrosarcoma
is_a
MONDO:0002678
pediatric fibrosarcoma
is_a
IFS
related
congenital fibrosarcoma
exact
infantile fibrosarcoma
exact
infantile fibrosarcoma (congenital fibrosarcoma)
exact
infantile fibrosarcoma (morphologic abnormality)
exact