endocardial fibroelastosis
Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.
MONDO:0016333
familial dilated cardiomyopathy
excluded_subClassOf
MONDO:0016338
non-familial dilated cardiomyopathy
excluded_subClassOf
MONDO:0016340
familial restrictive cardiomyopathy
excluded_subClassOf
MONDO:0016345
non-familial restrictive cardiomyopathy
excluded_subClassOf
MONDO:0000470
endocardium disorder
is_a
EFE
related
Elastomyofibrosis
exact
endocardial fibroelastosis
exact