double uterus-hemivagina-renal agenesis syndrome
Double uterus, hemivagina and renal agenesis is a rare congenital urogenital anomaly characterized by the presence of double uterus (didelphys, bicornuate or septum-complete or partial), unilateral cervico-vaginal obstruction (obstructed hemivagina-communicant, not communicant or septate and unilateral cervical atresia) and ipsilateral renal anomalies (renal agenesis and/or other urinary tract anomalies). Patients are usually diagnosed at puberty after menarche due to recurrent severe dysmenorrhea, chronic pelvic pain, excessive foul smelling mucopurulent discharge, spotting and intermenstrual bleeding (depending on the existence of uterine or vaginal communications). fever, dyspareunia, and a palpable abdominal, pelvic or vaginal mass (mucocolpos or pyocolpos) may also be present.
MONDO:0002254
syndromic disease
is_a
MONDO:0005039
reproductive system disorder
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MONDO:0021147
disorder of development or morphogenesis
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Double uterus and obstructed hemivagina syndrome
exact
Herlyn-Werner syndrome
exact
OHVIRA syndrome
exact
Wunderlich syndrome
exact
obstructed hemivagina and ipsilateral renal anomaly
exact