atypical coarctation of aorta
Middle aortic coarctation is a rare vascular anomaly characterized by the segmental narrowing of the abdominal and/or distal descending thoracic aorta with varying involvement of the visceral and renal arteries that commonly presents in children and young adults with early onset and refractory hypertension, abdominal angina, lower-limb claudication and that can lead to life-threatening complications associated with severe hypertension (i.e. myocardial infarction, heart failure, aortic rupture, renal insufficiency and intracranial hemorrhage). It may be due to various congenital or acquired causes, but it is most often secondary to an acquired inflammatory disease (i.e. Takayasu arteritis or giant cell arteritis).
MONDO:0007345
aorta coarctation
is_a
Midaortic syndrome
exact
coarctation of the abdominal aorta
exact
mid-aortic dysplastic syndrome
exact
mid-aortic syndrome
exact
middle aortic syndrome
exact