extraskeletal myxoid chondrosarcoma
A rare malignant soft tissue neoplasm of uncertain differentiation, characterized by the presence of chondroblast-like cells in a myxoid stroma and a multinodular growth pattern. The most common sites of involvement are the deep soft tissues of the extremities, particularly the thigh. It usually presents as an enlarging soft tissue mass. Patients may have long survivals, but local recurrences and metastases occur in approximately half of the cases. The most common site of metastasis is the lungs.
MONDO:0003847
hereditary disease
is_a
MONDO:0018078
soft tissue sarcoma
is_a
EMC
related
extraosseous chondrosarcoma
exact
extraskeletal chondrosarcoma
exact
myxoid extraosseous chondrosarcoma
exact
myxoid extraskeletal chondrosarcoma
exact