immunoglobulin G4-related sclerosing disease
A recently described mass-forming lesion that occurs in the pancreas, submandibular glands, lacrimal glands, lymph nodes, and hepatobiliary tract. It is characterized by the presence of marked tissue sclerosis and infiltration by numerous plasma cells. The plasma cells show immunohistochemical staining for IgG4 and the serum IgG4 levels are often increased.
MONDO:0007179
autoimmune disease
is_a
IgG4-RD
exact
IgG4-associated disease
related
IgG4-positive multiorgan lymphoproliferative syndrome
related
IgG4-related autoimmune disease
related
IgG4-related disease
exact
IgG4-related sclerosing disease
exact
IgG4-related systemic disease
exact
IgG4-related systemic sclerosing disease
related
IgG4-syndrome
related
hyper-IgG4 disease
related
immunoglobulin G4-related sclerosing disease
exact
multifocal fibrosclerosis
related
multifocal idiopathic fibrosclerosis
related
systemic IgG4-related plasmacytic syndrome
related
systemic IgG4-related sclerosing syndrome
related