adamantinoma
A low grade malignant neoplasm arising from the long bones. The tibia is the most frequently affected bone site. Patients present with swelling which may or may not be associated with pain. Morphologically, it is characterized by a biphasic pattern consisting of an epithelial and an osteofibrous component. The vast majority of cases recur if they are not treated with radical surgery. In a minority of cases the tumor may metastasize to other anatomic sites including lymph nodes, lungs, liver, brain, and skeleton.
MONDO:0015959
obsolete inherited syndrome with bone tumors as a major feature (obsolete MONDO:0015959)
excluded_subClassOf
MONDO:0002415
bone carcinoma
is_a
Extragnathic adamantinoma
exact
adamantinoma
exact
adamantinoma of long bones
exact
adamantinoma of long bones (morphologic abnormality)
exact
adamantinoma, malignant
exact
long bone adamantinoma
exact