sinus histiocytosis with massive lymphadenopathy
A rare disorder of unknown etiology characterized by distention of the lymph node sinuses and sinusoidal histiocytic infiltration. The histiocytes characteristically contain ingested lymphocytes. Patients present with cervical lymphadenopathy, fever, leukocytosis, and hypergammaglobulinemia. It can affect extranodal sites, including skin, bones, and the respiratory tract. It usually regresses spontaneously.
MONDO:0015531
non-Langerhans cell histiocytosis
is_a
Destombes-RosaC/-Dorfman disease
exact
Destombes-Rosaï-Dorfman disease
exact
RDD
exact
RosaC/-Dorfman-Destombes disease
exact
Rosai-Dorfman Disease
exact
Rosai-Dorfman disease
exact
Rosaï-Dorfman-Destombes disease
exact
SHML
exact
sinus histiocytosis with massive lymphadenopathy
exact