papillary renal cell carcinoma
A rare subtype of renal cell carcinoma, arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with hematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes, such as Hereditary leiomyoma renal cell carcinoma, Birt-Hogg-DubC) syndrome and Tuberous sclerosis, may predispose to the development of papillary renal cell carcinoma.
MONDO:0017891
obsolete inherited renal cancer-predisposing syndrome (obsolete MONDO:0017891)
excluded_subClassOf
MONDO:0002512
papillary adenocarcinoma
is_a
MONDO:0005549
renal cell adenocarcinoma
is_a
HPRCC
exact
RCCP
related
RCCP1
related
chromophil RCC
related
chromophil carcinoma of kidney
exact
chromophil carcinoma of the kidney
exact
chromophil renal cell carcinoma
exact
papillary (chromophil) renal cell carcinoma
exact
papillary renal carcinoma, malignant - (subtype)
related
papillary renal cell adenocarcinoma
exact
papillary renal cell cancer
exact
papillary renal cell carcinoma
exact
papillary renal cell carcinoma, bilateral - (subtype)
related
papillary renal cell carcinoma, familial - (subtype)
related
papillary renal cell carcinoma, multiple - (subtype)
related
papillary renal cell carcinoma, sporadic - (subtype)
related
renal adenocarcinoma
related
renal cell carcinoma, papillary, 1
related
renal cell carcinoma, papillary, type 1
exact
SPCC4B3.14