Dandy-Walker syndrome
Dandy-Walker malformation (DWM) is the association of three signs: hydrocephalus, partial or complete absence of the cerebellar vermis, and posterior fossa cyst contiguous with the fourth ventricle, presenting early in life with hydrocephalus, bulging occiput and posterior fossa signs such as cranial nerve palsies, nystagmus and ataxia.
MONDO:0002427
cerebellar disorder
is_a
MONDO:0020134
cystic malformation of the posterior fossa
is_a
DW complex
related
DWS
related
Dandy Walker Malformation
exact
Dandy-Walker complex
related
Dandy-Walker syndrome
exact
Dandy-Walker syndrome or malformation (type of DW complex)
related
Dandy-Walker syndrome, Isolated cases
exact
Dandy-Walker variant (type of DW complex)
related
mega cisterna magna (type of DW complex)
related