congenital pulmonary venous return anomaly
Congenital pulmonary venous return anomaly is a cardiac malformation where some or all of the pulmonary veins drain into the right atrium or the systemic veins, with or without the presence of pulmonary venous obstruction, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive congestive heart failure. The two main subtypes are congenital partial pulmonary venous return anomaly (PAPVC), where one or a few of the pulmonary veins are anomalous, and congenital total pulmonary venous return anomaly (TAPVC), where all of the pulmonary veins are anomalous.
MONDO:0020295
congenital pulmonary veins anomaly
is_a
APVR
related
TAPVR
related
TAPVR1
related
anomalous pulmonary venous return
related
congenital pulmonary venous connection anomaly
exact
pulmonary venous return anomaly
related
scimitar anomaly
related
scimitar syndrome
related
total anomalous pulmonary venous return
related