extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor
A spectrum of malignant tumors arising from the soft tissues, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. Pain and the presence of a mass are the most common clinical symptoms.
MONDO:0021038
Ewing sarcoma/peripheral primitive neuroectodermal tumor
is_a
extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumor
exact
extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumour
exact
extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumor
exact
extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumour
exact
extraosseous Ewing's tumour
related
extraosseous Ewings sarcoma-primitive neuroepithelial tumor
exact
extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor
exact