developmental and/or epileptic encephalopathy with spike-wave activation in sleep
A rare epileptic encephalopathy of childhood characterized by seizures, an electroencephalographic (EEG) pattern of electrical status epilepticus in sleep (ESES) and neurocognitive regression in at least 2 domains of development. This syndrome encompasses the previous syndromes epileptic encephalopathy with continuous spike-wave in sleep and atypical childhood epilepsy with centrotemporal spikes (also previously known as pseudo-Lennox syndrome and atypical benign partial epilepsy).
MONDO:0002254
syndromic disease
is_a
MONDO:0800500
childhood-onset epilepsy syndrome with developmental and/or epileptic encephalopathy
is_a
CSWS
exact
CSWSS syndrome
exact
DEE-SWAS
exact
EE-SWAS
exact
EESWAS
exact
ESES with language regression
exact
LK syndrome
exact
LKS
exact
continuous slow spike and wave of sleep
exact
continuous spike-wave during slow sleep syndrome
exact
continuous spike-wave in sleep
exact
continuous spikes and waves during sleep
exact
continuous spikes and waves during slow-wave sleep
exact
developmental and epileptic encephalopathy with spike-wave activation in sleep
exact
electrical status epilepticus of sleep
exact
electrographic status epilepticus in sleep
exact
electrographic status epilepticus of sleep
exact
epileptic aphasia
exact
epileptic encephalopathy with continuous spike-and-wave during slow sleep
exact
epileptic encephalopathy with spike and wave activation in sleep
exact
epileptic encephalopathy with spike-and-wave activation in sleep
exact
eses index
exact