superficial siderosis
Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in the spinal and cranial leptomeninges and subpial layer. The disease progresses slowly and patients may present with mild cognitive impairment, nystagmus, dysmetria, spasticity, dysdiadochokinesia, dysarthria, hyperreflexia, and Babinski signs. Additional features reported include dementia, urinary incontinence, anosmia, ageusia, and anisocoria.
MONDO:0016593
acquired ataxia
excluded_subClassOf
MONDO:0005559
neurodegenerative disease
is_a
hemosiderosis of the central nervous system
exact
superficial hemosiderosis of the CNS
exact
superficial hemosiderosis of the central nervous system
exact
superficial siderosis of the CNS
exact
superficial siderosis of the central nervous system
exact