PPoma
PPoma is a type of pancreatic endocrine tumor that hypersecretes pancreatic polypeptide (PP) but that does not cause a hypersecretion syndrome (is non-functioning) and instead presents with only non-specific symptoms such as weight loss, abdominal pain, jaundice, diarrhea and/or an abdominal mass, hence leading to a late diagnosis. PPoma can be associated with multiple endocrine neoplasia 1 (MEN-1).
MONDO:0019954
pancreatic neuroendocrine tumor
is_a
pancreatic polypeptide neoplasm
exact
pancreatic polypeptide tumor
exact
pancreatic polypeptide tumour
exact
pancreatic polypeptidoma
exact