atresia of small intestine
Atresia of small intestine is a special form of intestinal atresia with absence of mesentery, which is most likely due to an intrauterine intestinal vascular accident. Newborns are usually preterm infants with low birth-weights, that encounter feeding difficulties (including vomiting with initial feeds, which may later worsened and the abdomen becomes progressively distended) as well as failure to thrive. Affected children present disrupted bowel loops assuming a spiral configuration resembling an 'apple peel' and may have less than half of the normal length of the small bowel and a physiologically short bowel. Atresia of small intestine is characterized by jejunal atresia near the ligament of Treitz, foreshortened bowel, and a large mesenteric gap. The bowel distal to the atresia is precariously supplied. Atresia of small intestine may be a manifestation of cystic fibrosis. The most important cause of mortality is short bowel syndrome, encountered in 65% of cases.
MONDO:0021147
disorder of development or morphogenesis
is_a
MONDO:0024635
small intestine disorder
is_a
APSB
related
Jejunal Atresia
exact
Jejunoileal atresia
exact
apple peel syndrome
exact
apple-peel intestinal atresia
related
atresia of the small intestine
exact
congenital atresia of the small intestine
related
congenital small intestine atresia
exact
familial apple peel jejunal atresia
related
intestinal atresia type IIIb
exact
jejunal atresia
exact
small intestinal atresia
exact
small intestine atresia
exact