AL amyloidosis
Light chain amyloidosis
related
Light-chain amyloidosis
exact
amyloidosis AL
related
amyloidosis primary systemic
related
primary AL amyloidosis
related
primary amyloidosis
exact
primary systemic AL amyloidosis
related
primary systemic amyloidosis
related
systemic AL amyloidsis
related
AL Amyloidosis is a plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.
MONDO:0019724
obsolete secondary glomerular disease (obsolete MONDO:0019724)
excluded_subClassOf
MONDO:0005071
nervous system disorder
is_a
MONDO:0006504
acquired metabolic disease
is_a
MONDO:0016330
non-familial hypertrophic cardiomyopathy
is_a
MONDO:0016345
non-familial restrictive cardiomyopathy
is_a
MONDO:0019065
amyloidosis
is_a