sporadic infantile bilateral striatal necrosis
ABSN
exact
acute bilateral striatal necrosis
exact
sporadic IBSN
exact
sporadic infantile striatonigral degeneration
exact
sporadic infantile striatonigral necrosis
exact
Sporadic infantile bilateral necrosis is the sporadic form of infantile bilateral striatal necrosis (IBSN), a syndrome of bilateral symmetric spongy degeneration of the caudate nucleaus, putamen and globus pallidus characterized by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis.
MONDO:0015518
infantile bilateral striatal necrosis
is_a