Disease association ontology term - MONDO:0009329 - pulmonary venoocclusive disease 2
Term summary
- ID
- MONDO:0009329
- Name
- pulmonary venoocclusive disease 2
- Ontology or CV name
- Disease association
- Definition
- A rare form of pulmonary arterial hypertension (PAH) characterized by a capillary infiltration of the pulmonary interstitium, bronchioles and pleura leading to elevated pulmonary arterial resistance and right heart failure. PCH is potentially fatal.
