PomBase home

Disease association ontology term - MONDO:0015547 - hereditary dementia

Term summary

ID
MONDO:0015547
Name
hereditary dementia
Ontology or CV name
Disease association
Definition
An instance of dementia that is caused by an inherited genomic modification in an individual.

Parents

Annotation

Disease association

MONDO:0011397 - autosomal dominant cerebellar ataxia, deafness and narcolepsy

References:

Genes:

MONDO:0013886 - cerebellar dysfunction with variable cognitive and behavioral abnormalities

References:

Genes:

MONDO:0100087 - familial Alzheimer disease

References:

Genes:

MONDO:0014395 - frontotemporal dementia and/or amyotrophic lateral sclerosis 2

References:

Genes:

MONDO:0013501 - frontotemporal dementia and/or amyotrophic lateral sclerosis 6

References:

Genes:

MONDO:0010936 - frontotemporal dementia and/or amyotrophic lateral sclerosis 7

References:

Genes:

MONDO:0013584 - hereditary sensory neuropathy-deafness-dementia syndrome

References:

Genes:

MONDO:0000507 - inclusion body myopathy with Paget disease of bone and frontotemporal dementia

References:

Genes:

MONDO:0008178 - inclusion body myopathy with Paget disease of bone and frontotemporal dementia type 1

References:

Genes:

MONDO:0011706 - Kufor-Rakeb syndrome

References:

Genes:

MONDO:0018868 - metachromatic leukodystrophy

References:

Genes:

MONDO:0010476 - neurodegeneration with brain iron accumulation 5

References:

Genes:

MONDO:0014290 - neurodegeneration with brain iron accumulation 6

References:

Genes:

MONDO:0958231 - neurodevelopmental disorder with motor abnormalities, seizures, and facial dysmorphism

References:

Genes:

MONDO:0016163 - spinocerebellar ataxia 7

References:

Genes:

MONDO:0011330 - spinocerebellar ataxia type 10

References:

Genes:

MONDO:0011439 - spinocerebellar ataxia type 12

References:

Genes:

MONDO:0011781 - spinocerebellar ataxia type 17

References:

Genes:

MONDO:0008458 - spinocerebellar ataxia type 2

References:

Genes:

MONDO:0012246 - spinocerebellar ataxia type 26

References:

Genes:

MONDO:0012450 - spinocerebellar ataxia type 28

References:

Genes:

MONDO:0007574 - spinocerebellar ataxia type 34

References:

Genes:

MONDO:0013594 - spinocerebellar ataxia type 36

References:

Genes:

MONDO:0014417 - spinocerebellar ataxia type 38

References:

Genes:

MONDO:0008695 - VPS13A-related neurodegenerative disease

References:

Genes: