Disease association ontology term - MONDO:0018554 - pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
Term summary
- ID
- MONDO:0018554
- Name
- pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
- Ontology or CV name
- Disease association
- Definition
- A rare subgroup of pulmonary arterial hypertension (PAH) characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction.
