Disease association ontology term - MONDO:0019236 - inborn disorder of purine metabolism
Term summary
ID
MONDO:0019236
Name
inborn disorder of purine metabolism
Ontology or CV name
Disease association
Definition
An inherited metabolic disease that is has its basis in the disruption of purine nucleobase metabolic process.
Parents
is_a
inborn disorder of purine or pyrimidine metabolism
is_a
purine metabolism disease
Annotation
Disease association
MONDO:0013869
-
adenine phosphoribosyltransferase deficiency
References:
PB_REF:0000006
Genes:
apt1 (SPAC23A1.03)
MONDO:0007068
-
adenylosuccinate lyase deficiency
References:
PB_REF:0000006
Genes:
ade8 (SPBC14F5.09c)
MONDO:0012099
-
AICA-ribosiduria
References:
PB_REF:0000006
PMID:15114530
Genes:
ade10 (SPCPB16A4.03c)
MONDO:0010699
-
Charcot-Marie-Tooth disease X-linked recessive 5
References:
PB_REF:0000006
Genes:
prs5 (SPBC3D6.06c)
SPCC1620.06c
MONDO:0014719
-
developmental and epileptic encephalopathy, 35
References:
PB_REF:0000006
Genes:
ham1 (SPCC830.10)
MONDO:0010299
-
hypoxanthine guanine phosphoribosyltransferase partial deficiency
References:
PB_REF:0000006
Genes:
hpt1 (SPAC23C11.13c)
MONDO:0010298
-
Lesch-Nyhan syndrome
References:
PB_REF:0000006
PMID:23859867
Genes:
hpt1 (SPAC23C11.13c)
MONDO:0859003
-
PAICS deficiency
References:
PB_REF:0000006
Genes:
ade6 (SPCC1322.13)
ade7 (SPBC409.10)
MONDO:0010395
-
phosphoribosylpyrophosphate synthetase superactivity
References:
PB_REF:0000006
Genes:
prs5 (SPBC3D6.06c)
SPCC1620.06c
MONDO:0013171
-
purine nucleoside phosphorylase deficiency
References:
PB_REF:0000006
Genes:
SPAC1805.16c
MONDO:0007064
-
severe combined immunodeficiency, autosomal recessive, T cell-negative, B cell-negative, NK cell-negative, due to adenosine deaminase deficiency
References:
PB_REF:0000006
Genes:
dea2 (SPBC1198.02)